I wanted to write an event preview for a great night at Blue Mountain this weekend. The line-up is wicked, and I’m really looking forward to it.
It’s only £5 Entry and that’s 15 DJ’s and 12 MC’s…
However, before that I want to explain a bit about why the night has been put on, and about the woman, Laura, who has been tirelessly and amazingly working to put this event (and many other events around Bristol) together.
Laura’s son Liam was unexpectedly diagnosed with Freidriech’s Ataxia a few short months ago.
Laura Rice is a good friend of mine, and an amazing woman and wonderful mother to three. We met working in a slightly dodgy pub in Fishponds – my first job in Bristol – so it was great to meet a friendly face! We have worked together in various other pubs since. She is a hard worker, and one of the most caring people I know.
This February, her son Liam was diagnosed with a rare inherited disease caused by a defective or mutated gene, causing damage to the nervous system.
Freidriech’s Ataxia is hereditary, but the chances of an individual being affected are tiny (about 1 in 50,000) as in order to contract the disease both partners must unknowingly have the same defective gene. Neither parent is affected by the disease, they are simply carriers. Even in the rare case of both parents having the defective gene, there is only a 1 in 4 chance of the child being affected.
Freidriech’s Ataxia initially leads to impaired muscle coordination, impaired sensory function and eventually to loss of feeling and reflex, heart problems, scoliosis, and the slowing and slurring of speech.
The disease does not affect the cognitive functions, i.e., the sufferer’s thinking is not impaired, but they can be left totally incapacitated.
There is currently no known cure for the disease, however advanced research and understanding of genetics is leading to breakthroughs in treatment.
The life of the sufferer can however be vastly improved in various ways. Clinical trials, physical therapy, braces and surgery on the spine and feet, speech therapy and medication that treats heart disease and diabetes (which is a common complication of the disease) can all help to extend a functional life.
Liam is ten years old, and without raising money for these treatments, as well as enabling his family to support him and make life as comfortable as they can, he may be wheelchair-bound within ten years.
Laura and her husband Matt (with help from many of their friends, and despite the recent and obviously devastating news) have been concentrating on the organisation of events and working tirelessly to raise both awareness and money for the condition.
The biggest event so far is being held on Saturday August 4th at Blue Mountain Bristol. All the DJ’s, MC’s and the venue have kindly donated their time, talent and effort for free, and as I said, the night looks great.
All you have to do is come down, have a wicked night, and chuck some money in the collection. What could be easier than that?!
So…now I’ve done the explaining, let’s tell you about the night!
Jungle, Drum n Bass, Oldskool, Hardcore headlined by Nicky Blackmarket & Joey Riot
Kickback & Vinyljunkie/Chris Fear/Rusher & Fox/Ineffect/Dyson & Chewy/DJ Probe to name just a few…
As well as twelve MC’s.
That’s a lot of good stuff for £5, and it really is for a good cause.<p